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Eur J Dent. 2010 Apr;4(2):215-22.

Ectodermal dysplasia with anodontia: a report of two cases.

Author information

  • 1DDS, Research Assistant, Gazi University, Faculty of Dentistry, Department of Paediatric Dentistry, Ankara, Turkey.

Abstract

Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances in the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. Two case reports illustrating the prosthetic rehabilitation of 2 young boys with anhidrotic ectodermal dysplasia associated with severe anodontia are presented. Since the oral rehabilitation of these cases is often difficult; particularly in pediatric patients, treatment should be administered by a multidisciplinary team involving pediatric dentistry, orthodontics, prosthodontics and oral-maxillofacial surgery.

KEYWORDS:

Anodontia; Ectodermal dysplasia; Multidisciplinary management; Prosthetic rehabilitation

PMID:
20396456
[PubMed]
PMCID:
PMC2853819
Free PMC Article

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