Pacing Clin Electrophysiol. 2010 May;33(5):618-9. Epub 2010 Mar 8.

A young patient with Danon disease receives two ICD shocks: why?

Source

Hôpital Trousseau, Cardiology, Tours, France. nourazannad@sfr.fr

Abstract

We report the case of an 18-year-old man with Danon disease, a genetic disorder inclunding a severe hypertrophic cardiomyopathy with very broad QRS, who had an implantable cardioverter defibrillator for primary prevention. Nine months after implantation, he received two inappropriate shocks due to R-wave double counting during sinus tachycardia. We discuss how to avoid such inappropriate therapy.

PMID:: 20230469; [PubMed - indexed for MEDLINE]

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