Three cases of granular cell myoblastoma occurring in the Igbos of Nigeria are reported. In this ethnic group the tumor has shown several typical features as follows: it is rarely diagnosed preoperatively; it is found more frequently in the oral cavity and breast than in most other sites; and it is in the maxilla of girls that it usually presents congenitally. A unique presentation in this ethnic group occurred in the perineum. The lesion found in this site appears to be the first to be reported in the literature.