Idiopathic hypertrophic cranial pachymeningitis and dural sinus occlusion: two patients with long-term follow up

J Clin Neurosci. 2009 Jul;16(7):937-42. doi: 10.1016/j.jocn.2008.08.012. Epub 2009 Apr 17.

Abstract

Idiopathic hypertrophic cranial pachymeningitis (IHPM) is a clinicopathological entity characterized by thickening and fibrosis of the dura mater with resultant clinical symptoms. It is generally steroid responsive and has a tendency to remit and relapse. We present here two patients with IHPM with associated dural sinus occlusion and describe their clinicoradiological features and long-term course and outcome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cardiovascular Diseases / complications*
  • Cardiovascular Diseases / pathology
  • Cerebral Angiography / methods
  • Cranial Sinuses / pathology*
  • Dura Mater / pathology*
  • Humans
  • Hypertrophy
  • Longitudinal Studies
  • Magnetic Resonance Imaging / methods
  • Male
  • Meningitis / complications*
  • Meningitis / pathology
  • Young Adult