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Am J Surg Pathol. 1991 Oct;15(10):935-41.

Solitary congenital fibromatosis (infantile myofibromatosis) of bone.

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  • 1Section of Surgical Pathology, Mayo Clinic, Rochester, MN 55905.

Abstract

Congenital fibromatosis is a rare and benign myofibroblastic tumor that may occur in either a solitary or multicentric form. The soft-tissue form of this entity is well recognized. This report analyzes the clinical and pathologic features of 14 cases of congenital fibromatosis in which the tumor existed as a solitary lesion in bone. Most of the tumors (71%) were in patients who were 2 years old or younger. All but one tumor involved the craniofacial bones. Radiographically, they were purely lucent lesions in which a sclerotic rim was visible in each skull lesion. The myofibroblastic appearance closely resembled the microscopic features seen in the soft-tissue counterpart. For appropriate surgical management, it is imperative to recognize that this tumor occurs as a solitary lesion in bone and that it is distinct from other, more aggressive fibrous lesions.

PMID:
1928549
[PubMed - indexed for MEDLINE]
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