True teratomas of the nasopharynx are rare tumors of the newborn. Surgical resection is the treatment of choice. We describe two patients with this entity. The first patient has undergone follow-up for over 10 years, while the second patient was evaluated with fine-needle aspiration and magnetic resonance imaging. The advantages of these studies and alternate surgical techniques are discussed. Of interest is the fact that both patients may have had central nervous system abnormalities.