The myofibroblastic tumor (MFT) is a very rare tumor, initially described in the lungs, and which involves exceptionally the heart. We report the unusual case of a 31 year-old female patient, in whom the tumor produced a bilateral pulmonary embolism and whose unique clinical demonstration was a longstanding fever. The tumor, located in the right ventricle, has been surgically completely excised with excellent results. We also make a review of literature of the various aspects of this pathology.