Abstract
A 3-month-old infant presented in extremis with a flail tricuspid valve. The authors theorized that the genesis of her papillary muscle rupture was perinatal ischemia compounded by worsening pulmonary valvular stenosis leading to excessive fiber tension. Her underlying diagnosis of autoimmune-mediated heart block with endocardial fibroelastosis and prenatal glucocorticoid steroid treatment represents potentiating factors.
MeSH terms
-
Cardiac Surgical Procedures / methods
-
Cardiomyopathies / complications*
-
Cardiomyopathies / diagnostic imaging
-
Cardiomyopathies / surgery
-
Diagnosis, Differential
-
Echocardiography, Doppler, Color
-
Female
-
Follow-Up Studies
-
Humans
-
Infant
-
Papillary Muscles*
-
Rupture, Spontaneous
-
Suture Techniques
-
Tricuspid Valve Insufficiency / diagnostic imaging
-
Tricuspid Valve Insufficiency / etiology*
-
Tricuspid Valve Insufficiency / surgery