Pediatr Transplant. 2007 May;11(3):327-31.

Successful cardiac transplantation in Barth syndrome--single-centre experience of four patients.

Mangat J, Lunnon-Wood T, Rees P, Elliott M, Burch M.

Source

Cardiac Transplant, Great Ormond Street Hospital, London, UK.

Abstract

We describe four patients with Barth syndrome who have undergone successful orthotopic heart transplantation. Patients are one, seven, 12.5 and 14.7 yr post-transplantation. One episode of severe infection occurred. Renal dysfunction and coronary allograft vasculopathy do not appear accelerated over non-Barth patients. Despite withholding purine synthesis inhibitors, these patients have not demonstrated an increased rate of rejection.

PMID:: 17430492; [PubMed - indexed for MEDLINE]

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