Accumulation of N-terminal mutant huntingtin in mouse and monkey models implicated as a pathogenic mechanism in Huntington's disease.
Wang CE, Tydlacka S, Orr AL, Yang SH, Graham RK, Hayden MR, Li S, Chan AW, Li XJ.
Hum Mol Genet. 2008 Sep 1; 17(17):2738-51. Epub 2008 Jun 16.
[Hum Mol Genet. 2008]