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    AJNR Am J Neuroradiol. 2006 Feb;27(2):274-7.

    Oromaxillofacial osseous abnormality in Sturge-Weber syndrome: case report and review of the literature.

    Source

    Division of Neuroradiology, Russell H. Morgan Department of Radiology and Radiological Science, Johns Hopkins University School of Medicine, Baltimore, MD 21287, USA.

    Abstract

    We report a case of a 17-month-old child affected by Sturge-Weber syndrome who had unusually rapid overgrowth of the left frontal, temporal, orbital, and maxillary regions. CT angiography illustrated osteohypertrophy with periostitis and associated soft tissue hypertrophy directly corresponding to the distribution of the cutaneous port-wine stain. Extended maxillectomy was performed because of rapid growth and clinical debilitation, with surgical pathology revealing juvenile ossifying fibroma.

    PMID:
    16484391
    [PubMed - indexed for MEDLINE]
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