Pediatr Crit Care Med. 2006 Mar;7(2):177-9.

Late presentation of alveolar capillary dysplasia in an infant.

Shankar V, Haque A, Johnson J, Pietsch J.

Source

Divisions of Pediatric Critical Care Medicine, Monroe Carell Jr. Children's Hospital at Vanderbilt, Nashville, TN, USA.

Abstract

OBJECTIVE:

To report a case of late presentation of alveolar capillary dysplasia and misalignment of pulmonary veins.

DESIGN:

Descriptive case report.

SETTING:

Pediatric intensive care unit of a tertiary care children's hospital.

PATIENT:

Seven-week-old female infant with severe hypoxemic respiratory failure.

CONCLUSION:

Alveolar capillary dysplasia with misalignment of pulmonary veins is a cause of primary pulmonary hypertension in newborns that can rarely present past the newborn period. Early lung biopsy can be helpful in establishing the diagnosis and avoiding ineffective, futile, and expensive therapeutic interventions.

PMID:: 16474258; [PubMed - indexed for MEDLINE]

Publication Types, MeSH Terms

Publication Types

Case Reports

MeSH Terms

LinkOut - more resources

Full Text Sources

Medical

Supplemental Content

Related citations

Alveolar capillary dysplasia with congenital misalignment of pulmonary vessels. [Asian Cardiovasc Thorac Ann. 2005]
Alveolar capillary dysplasia with congenital misalignment of pulmonary vessels.
Sihoe AD, Lee AT, To KF, Thung KH, Lee TW, Yim AP. Asian Cardiovasc Thorac Ann. 2005 Mar; 13(1):82-4.
Omphalocele and alveolar capillary dysplasia: a new association. [Pediatr Crit Care Med. 2010]
Omphalocele and alveolar capillary dysplasia: a new association.
Gerrits LC, De Mol AC, Bulten J, Van der Staak FH, Van Heijst AF. Pediatr Crit Care Med. 2010 May; 11(3):e36-7.
Profound hypoxemia and pulmonary hypertension in a 7-month-old infant: late presentation of alveolar capillary dysplasia. [Pediatr Crit Care Med. 2008]
Profound hypoxemia and pulmonary hypertension in a 7-month-old infant: late presentation of alveolar capillary dysplasia.
Ahmed S, Ackerman V, Faught P, Langston C. Pediatr Crit Care Med. 2008 Nov; 9(6):e43-6.
Review Congenital alveolar capillary dysplasia with misalignment of pulmonary veins associated with hypoplastic left heart syndrome. [Pediatr Dev Pathol. 2001]
Review Congenital alveolar capillary dysplasia with misalignment of pulmonary veins associated with hypoplastic left heart syndrome.
Rabah R, Poulik JM. Pediatr Dev Pathol. 2001 Mar-Apr; 4(2):167-74.
Review Alveolar capillary dysplasia. Report of a case of prolonged life without extracorporeal membrane oxygenation (ECMO) and review of the literature. [Early Hum Dev. 2000]
Review Alveolar capillary dysplasia. Report of a case of prolonged life without extracorporeal membrane oxygenation (ECMO) and review of the literature.
Al-Hathlol K, Phillips S, MK Seshia, Casiro O, Alvaro RE, Rigatto H. Early Hum Dev. 2000 Feb; 57(2):85-94.

See reviews... See all...

Cited by 1 PubMed Central article

Genetic Basis of Children's Interstitial Lung Disease. [Pediatr Allergy Immunol Pulmonol. 2010]
Genetic Basis of Children's Interstitial Lung Disease.
Nogee LM. Pediatr Allergy Immunol Pulmonol. 2010 Mar; 23(1):15-24.

Related information

Related Citations
Calculated set of PubMed citations closely related to the selected article(s) retrieved using a word weight algorithm. Related articles are displayed in ranked order from most to least relevant, with the “linked from” citation displayed first.
OMIM (calculated)
Online Mendelian Inheritance in Man (OMIM) records that include the current articles as references in the light bulb links within or in the citations at the end of the OMIM record. The references available through the light bulb link are collected using the PubMed related articles algorithm to identify records with similar terminology to the OMIM record.
Cited in PMC
Full-text articles in the PubMed Central Database that cite the current articles.

Recent activity

Clear Turn Off Turn On

Late presentation of alveolar capillary dysplasia in an infant.
Late presentation of alveolar capillary dysplasia in an infant.
Pediatr Crit Care Med. 2006 Mar ;7(2):177-9.

PubMed
Articular cartilage repair in the adolescent athlete: is autologous chondrocyte ...
Articular cartilage repair in the adolescent athlete: is autologous chondrocyte implantation the answer?
Clin J Sport Med. 2006 Nov ;16(6):465-70.

PubMed
Soft tissue sleeve approach to open reduction and internal fixation of proximal ...
Soft tissue sleeve approach to open reduction and internal fixation of proximal phalangeal fractures.
Tech Hand Up Extrem Surg. 2008 Sep ;12(3):161-5.

PubMed
Synthesis of C14-17-hydroxy-11-desoxycorticosterone and 17-hydroxycorticosterone...
Synthesis of C14-17-hydroxy-11-desoxycorticosterone and 17-hydroxycorticosterone by fractionated extracts of adrenal homogenates.
Arch Biochem Biophys. 1953 Feb ;42(2):477-8.

PubMed
Metastatic potential of melanomas defined by specific gene expression profiles w...
Metastatic potential of melanomas defined by specific gene expression profiles with no BRAF signature.
Pigment Cell Res. 2006 Aug ;19(4):290-302.

PubMed

Your browsing activity is empty.

Activity recording is turned off.

Turn recording back on

PubMed

Display Settings:

Send to: