Decreased mitochondrial oxidative capacity in hereditary tyrosinemia type 1

Scand J Gastroenterol. 2005 May;40(5):612-3. doi: 10.1080/00365520510015548.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Aminopyrine / metabolism
  • Carbon Isotopes
  • Child
  • Female
  • Humans
  • Mitochondria, Liver / metabolism*
  • Oxidation-Reduction
  • Oxygen Consumption
  • Tyrosinemias / genetics*
  • Tyrosinemias / metabolism

Substances

  • Carbon Isotopes
  • Aminopyrine