[Benign paroxysmal tonic upgaze of infancy: 2 additional cases]

Servide de pédiatrie, Hôtel-Dieu, 63000 Clermont-Ferrand, France. frouveyrol@chu-clermontferrand.fr

Benign paroxysmal tonic upgaze is an ill-defined neuro-ophthalmological disorder with onset in infancy. It consists of sudden ocular movements with sustained upward deviation of the eyes. Episodes disappear with time: spontaneous remission occurs within a few months or years without any change in psychomotor development. EEG and neuro-imaging are unrevealing. To date, the pathogenesis of the condition is still unknown. Early recognition of this benign condition minimizes potentially unnecessary investigations and treatments. Herein, we report on 2 additional sporadic cases.

PMID: 12915017 [PubMed - indexed for MEDLINE]