Is severe deficiency of ADAMTS-13 specific for thrombotic thrombocytopenic purpura? Yes

J Thromb Haemost. 2003 Apr;1(4):625-31. doi: 10.1046/j.1538-7836.2003.00169.x.
No abstract available

Publication types

  • Research Support, U.S. Gov't, P.H.S.
  • Review

MeSH terms

  • ADAM Proteins
  • ADAMTS13 Protein
  • Humans
  • Metalloendopeptidases / deficiency*
  • Metalloendopeptidases / genetics
  • Mutation
  • Purpura, Thrombotic Thrombocytopenic / enzymology
  • Purpura, Thrombotic Thrombocytopenic / etiology*
  • von Willebrand Factor / metabolism

Substances

  • von Willebrand Factor
  • ADAM Proteins
  • Metalloendopeptidases
  • ADAMTS13 Protein
  • ADAMTS13 protein, human