No abstract available
MeSH terms
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Chronic Disease
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Cystic Fibrosis / complications*
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Cystic Fibrosis / genetics
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Cystic Fibrosis / immunology
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Cystic Fibrosis / metabolism
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Cystic Fibrosis Transmembrane Conductance Regulator / genetics
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Cystic Fibrosis Transmembrane Conductance Regulator / metabolism
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Genetic Therapy / methods
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Humans
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Ion Transport / physiology
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Lung Transplantation
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Neutrophil Activation
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Protein Processing, Post-Translational
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Respiratory Mucosa / metabolism
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Respiratory Tract Infections / etiology*
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Respiratory Tract Infections / immunology
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Respiratory Tract Infections / prevention & control
Substances
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CFTR protein, human
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Cystic Fibrosis Transmembrane Conductance Regulator