Treatment of progressive metastatic glomus jugulare tumor (paraganglioma) with gemcitabine

Neuro Oncol. 2000 Jul;2(3):190-1. doi: 10.1093/neuonc/2.3.190.

Abstract

Paragangliomas are rare tumors of the paraganglia composed of specialized neural crest cells arising in association with sympathetic ganglia. Here we report a case of progressive, metastatic paraganglioma (glomus jugulare tumor) responsive to single agent gemcitabine. In addition, a brief review of chemotherapy for paraganglioma follows the case presentation.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Antimetabolites, Antineoplastic / therapeutic use*
  • Brain Neoplasms / diagnosis
  • Brain Neoplasms / pathology*
  • Deoxycytidine / analogs & derivatives
  • Deoxycytidine / therapeutic use*
  • Female
  • Gemcitabine
  • Humans
  • Lung Neoplasms / diagnosis
  • Lung Neoplasms / drug therapy*
  • Lung Neoplasms / secondary*
  • Magnetic Resonance Imaging
  • Paraganglioma / diagnosis
  • Paraganglioma / drug therapy*
  • Paraganglioma / secondary*
  • Tomography, X-Ray Computed

Substances

  • Antimetabolites, Antineoplastic
  • Deoxycytidine
  • Gemcitabine