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West J Med. Oct 1996; 165(4): 231–233.
PMCID: PMC1303758

Lysinuric protein intolerance presenting as coma in a middle-aged man.

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Selected References

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  • Rajantie J, Simell O, Rapola J, Perheentupa J. Lysinuric protein intolerance: a two-year trial of dietary supplementation therapy with citrulline and lysine. J Pediatr. 1980 Dec;97(6):927–932. [PubMed]
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  • Fakler CR, Kaftan HA, Nelin LD. Two cases suggesting a role for the L-arginine nitric oxide pathway in neonatal blood pressure regulation. Acta Paediatr. 1995 Apr;84(4):460–462. [PubMed]
  • Wakabayashi Y, Yamada E, Yoshida T, Takahashi H. Deficiency of endogenous arginine synthesis provokes hypertension by exhausting substrate arginine for nitric oxide synthesis. Biochem Biophys Res Commun. 1994 Dec 15;205(2):1391–1398. [PubMed]

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