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Pulmonary interstitial glycogenosis

MedGen UID:
798843
Concept ID:
CN201153
Finding
Synonyms: Infantile cellular interstitial pneumonitis; PIG
Modes of inheritance:
not inherited
MedGen UID:
832438
Concept ID:
CN227390
Intellectual Product
Describes a disorder that is not inherited.
 
Orphanet: ORPHA217557

Definition

Pulmonary interstitial glycogenosis (PIG) is a rare non-lethal pediatric form of interstitial lung disease (ILD, see this term). [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews
  • CROGPulmonary interstitial glycogenosis

Recent clinical studies

Etiology

Citti A, Peca D, Petrini S, Cutrera R, Biban P, Haass C, Boldrini R, Danhaive O
Ultrastruct Pathol 2013 Oct;37(5):356-65. doi: 10.3109/01913123.2013.811454. PMID: 24047351
Popler J, Lesnick B, Dishop MK, Deterding RR
Chest 2012 Sep;142(3):774-80. doi: 10.1378/chest.12-0492. PMID: 22948581
Dishop MK
Paediatr Respir Rev 2011 Dec;12(4):230-7. Epub 2011 Mar 5 doi: 10.1016/j.prrv.2011.01.002. [Epub ahead of print] PMID: 22018036
Langston C, Dishop MK
Pediatr Dev Pathol 2009 Nov-Dec;12(6):421-37. doi: 10.2350/08-11-0559.1. PMID: 19323600
Canakis AM, Cutz E, Manson D, O'Brodovich H
Am J Respir Crit Care Med 2002 Jun 1;165(11):1557-65. doi: 10.1164/rccm.2105139. PMID: 12045133

Diagnosis

Ross MK, Ellis LS, Bird LM, Hagood JS
Pediatr Pulmonol 2014 May;49(5):508-11. Epub 2013 Sep 3 doi: 10.1002/ppul.22871. [Epub ahead of print] PMID: 24039098
Ehsan Z, Montgomery GS, Tiller C, Kisling J, Chang DV, Tepper RS
Pediatr Pulmonol 2014 Mar;49(3):E17-20. Epub 2013 Feb 8 doi: 10.1002/ppul.22738. [Epub ahead of print] PMID: 23401236
Radman MR, Goldhoff P, Jones KD, Azakie A, Datar S, Adatia I, Oishi PE, Fineman JR
Pediatr Cardiol 2013 Jun;34(5):1254-7. Epub 2012 May 22 doi: 10.1007/s00246-012-0371-z. [Epub ahead of print] PMID: 22614905Free PMC Article
Alkhorayyef A, Ryerson L, Chan A, Phillipos E, Lacson A, Adatia I
Pediatr Cardiol 2013 Feb;34(2):462-6. Epub 2012 Mar 28 doi: 10.1007/s00246-012-0311-y. [Epub ahead of print] PMID: 22453840
King BA, Boyd JT, Kingma PS
Pediatr Pulmonol 2011 Nov;46(11):1142-5. Epub 2011 May 26 doi: 10.1002/ppul.21486. [Epub ahead of print] PMID: 21618718Free PMC Article

Therapy

Ehsan Z, Montgomery GS, Tiller C, Kisling J, Chang DV, Tepper RS
Pediatr Pulmonol 2014 Mar;49(3):E17-20. Epub 2013 Feb 8 doi: 10.1002/ppul.22738. [Epub ahead of print] PMID: 23401236
Deutsch GH, Young LR
Pediatr Dev Pathol 2009 Nov-Dec;12(6):475-80. doi: 10.2350/08-12-0575.1. PMID: 19320535
Deutsch GH, Young LR, Deterding RR, Fan LL, Dell SD, Bean JA, Brody AS, Nogee LM, Trapnell BC, Langston C; Pathology Cooperative Group, Albright EA, Askin FB, Baker P, Chou PM, Cool CM, Coventry SC, Cutz E, Davis MM, Dishop MK, Galambos C, Patterson K, Travis WD, Wert SE, White FV; ChILD Research Co-operative
Am J Respir Crit Care Med 2007 Dec 1;176(11):1120-8. Epub 2007 Sep 20 doi: 10.1164/rccm.200703-393OC. [Epub ahead of print] PMID: 17885266Free PMC Article
Canakis AM, Cutz E, Manson D, O'Brodovich H
Am J Respir Crit Care Med 2002 Jun 1;165(11):1557-65. doi: 10.1164/rccm.2105139. PMID: 12045133

Prognosis

Alkhorayyef A, Ryerson L, Chan A, Phillipos E, Lacson A, Adatia I
Pediatr Cardiol 2013 Feb;34(2):462-6. Epub 2012 Mar 28 doi: 10.1007/s00246-012-0311-y. [Epub ahead of print] PMID: 22453840
King BA, Boyd JT, Kingma PS
Pediatr Pulmonol 2011 Nov;46(11):1142-5. Epub 2011 May 26 doi: 10.1002/ppul.21486. [Epub ahead of print] PMID: 21618718Free PMC Article
Lanfranchi M, Allbery SM, Wheelock L, Perry D
Pediatr Radiol 2010 Mar;40(3):361-5. Epub 2009 Nov 10 doi: 10.1007/s00247-009-1455-7. [Epub ahead of print] PMID: 19902199
Deutsch GH, Young LR
Pediatr Dev Pathol 2009 Nov-Dec;12(6):475-80. doi: 10.2350/08-12-0575.1. PMID: 19320535
Canakis AM, Cutz E, Manson D, O'Brodovich H
Am J Respir Crit Care Med 2002 Jun 1;165(11):1557-65. doi: 10.1164/rccm.2105139. PMID: 12045133

Clinical prediction guides

Ehsan Z, Montgomery GS, Tiller C, Kisling J, Chang DV, Tepper RS
Pediatr Pulmonol 2014 Mar;49(3):E17-20. Epub 2013 Feb 8 doi: 10.1002/ppul.22738. [Epub ahead of print] PMID: 23401236

Recent systematic reviews

Citti A, Peca D, Petrini S, Cutrera R, Biban P, Haass C, Boldrini R, Danhaive O
Ultrastruct Pathol 2013 Oct;37(5):356-65. doi: 10.3109/01913123.2013.811454. PMID: 24047351

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