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Congenital cystic adenomatoid malformation of the lung

MedGen UID:
506423
Concept ID:
CN116692
Finding
Synonyms: CCAM; Congenital cystic disease of the lung; Cystic adenomatoid lung disease
 
HPO: HP:0010959

Definition

Congenital cystic adenomatoid malformation (CCAM) can be diagnosed prenatally if ultrasound shows a cystic or solid lung tumor. A CCAM does not have systemic arterial blood supply (in contrast to bronchopulmonary sequenstration). It is a cystic area within the lung that originates from abnormal embryogenesis. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews
  • CROGCongenital cystic adenomatoid malformation of the lung

Conditions with this feature

Young's syndrome
MedGen UID:
137934
Concept ID:
C0340037
Disease or Syndrome
Young syndrome is characterized by chronic sinopulmonary infections, persistent azoospermia, and normal spermatogenesis (Handelsman et al., 1984).
BOD syndrome
MedGen UID:
350585
Concept ID:
C1862082
Disease or Syndrome

Recent clinical studies

Etiology

Lima JS, Camargos PA, Aguiar RA, Campos AS, Aguiar MJ
J Matern Fetal Neonatal Med 2014 Feb;27(3):228-32. Epub 2013 Jul 10 doi: 10.3109/14767058.2013.807236. [Epub ahead of print] PMID: 23697759
Tsai HF, Cheng YC, Ko HC, Kang L, Tsai PY, Yu CH, Chang CH, Chang FM
Taiwan J Obstet Gynecol 2013 Mar;52(1):90-6. doi: 10.1016/j.tjog.2012.10.004. PMID: 23548226
Liao SL, Lai SH, Hsueh C, Wong KS
Chang Gung Med J 2010 Jan-Feb;33(1):36-43. PMID: 20184793
Nagata K, Masumoto K, Tesiba R, Esumi G, Tsukimori K, Norio W, Taguchi T
Pediatr Surg Int 2009 Sep;25(9):753-7. doi: 10.1007/s00383-009-2431-x. PMID: 19662430
Conforti A, Aloi I, Trucchi A, Morini F, Nahom A, Inserra A, Bagolan P
J Thorac Cardiovasc Surg 2009 Oct;138(4):826-30. Epub 2009 Mar 26 doi: 10.1016/j.jtcvs.2009.01.014. [Epub ahead of print] PMID: 19660296

Diagnosis

Lima JS, Camargos PA, Aguiar RA, Campos AS, Aguiar MJ
J Matern Fetal Neonatal Med 2014 Feb;27(3):228-32. Epub 2013 Jul 10 doi: 10.3109/14767058.2013.807236. [Epub ahead of print] PMID: 23697759
Chen CP, Chang TY, Guo WY, Su YN, Chen YY, Chern SR, Su JW, Wang W
Taiwan J Obstet Gynecol 2013 Sep;52(3):415-9. doi: 10.1016/j.tjog.2013.05.002. PMID: 24075384
Tsai HF, Cheng YC, Ko HC, Kang L, Tsai PY, Yu CH, Chang CH, Chang FM
Taiwan J Obstet Gynecol 2013 Mar;52(1):90-6. doi: 10.1016/j.tjog.2012.10.004. PMID: 23548226
Sa YJ, Kim YD, Moon SW, Kim CK, Ki CS
Surg Today 2013 Dec;43(12):1467-9. Epub 2012 Oct 5 doi: 10.1007/s00595-012-0355-x. [Epub ahead of print] PMID: 23052746
Patella M, Anile M, Diso D, Onorati I, Venuta F
Lung 2012 Dec;190(6):697-8. Epub 2012 Jul 8 doi: 10.1007/s00408-012-9402-z. [Epub ahead of print] PMID: 22773247

Therapy

Nasr A, Bass J
J Pediatr Surg 2012 May;47(5):857-61. doi: 10.1016/j.jpedsurg.2012.01.036. PMID: 22595561
Rocha G, Fernandes PC, Proença E, Quintas C, Martins T, Azevedo I, Guimarães H
Rev Port Pneumol 2007 Jul-Aug;13(4):511-23. PMID: 17898911
Asabe K, Oka Y, Shirakusa T
Congenit Anom (Kyoto) 2005 Sep;45(3):96-101. doi: 10.1111/j.1741-4520.2005.00075.x. PMID: 16131368
Levison J, Van Asperen P, Wong C, Harvey J, Halliday R
J Paediatr Child Health 2004 Aug;40(8):474-6. doi: 10.1111/j.1440-1754.2004.00433.x. PMID: 15265191
Huang HJ, Talbot AR, Liu KC, Chen CP, Fang HY
Ann Thorac Surg 2004 Jul;78(1):337-9. doi: 10.1016/S0003-4975(03)01289-X. PMID: 15223463

Prognosis

Lima JS, Camargos PA, Aguiar RA, Campos AS, Aguiar MJ
J Matern Fetal Neonatal Med 2014 Feb;27(3):228-32. Epub 2013 Jul 10 doi: 10.3109/14767058.2013.807236. [Epub ahead of print] PMID: 23697759
Zawiejska A, Pietryga M, Wender-Ozegowska E, Brazert K, Brazert J
Ginekol Pol 2009 Aug;80(8):624-8. PMID: 19824463
Nagata K, Masumoto K, Tesiba R, Esumi G, Tsukimori K, Norio W, Taguchi T
Pediatr Surg Int 2009 Sep;25(9):753-7. doi: 10.1007/s00383-009-2431-x. PMID: 19662430
Lo AY, Jones S
J Pediatr Surg 2008 May;43(5):797-9. doi: 10.1016/j.jpedsurg.2007.12.016. PMID: 18485941
Calvert JK, Boyd PA, Chamberlain PC, Syed S, Lakhoo K
Arch Dis Child Fetal Neonatal Ed 2006 Jan;91(1):F26-8. Epub 2005 Aug 30 doi: 10.1136/adc.2004.068866. [Epub ahead of print] PMID: 16131533Free PMC Article

Clinical prediction guides

Lima JS, Camargos PA, Aguiar RA, Campos AS, Aguiar MJ
J Matern Fetal Neonatal Med 2014 Feb;27(3):228-32. Epub 2013 Jul 10 doi: 10.3109/14767058.2013.807236. [Epub ahead of print] PMID: 23697759
Liao SL, Lai SH, Hsueh C, Wong KS
Chang Gung Med J 2010 Jan-Feb;33(1):36-43. PMID: 20184793
Nagata K, Masumoto K, Tesiba R, Esumi G, Tsukimori K, Norio W, Taguchi T
Pediatr Surg Int 2009 Sep;25(9):753-7. doi: 10.1007/s00383-009-2431-x. PMID: 19662430
Roberts D, Sweeney E, Walkinshaw S
Fetal Diagn Ther 2001 Mar-Apr;16(2):65-7. doi: 53884. PMID: 11173951
De Santis M, Masini L, Noia G, Cavaliere AF, Oliva N, Caruso A
Fetal Diagn Ther 2000 Jul-Aug;15(4):246-50. doi: 21015. PMID: 10867488

Recent systematic reviews

Nasr A, Bass J
J Pediatr Surg 2012 May;47(5):857-61. doi: 10.1016/j.jpedsurg.2012.01.036. PMID: 22595561

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