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Ventricular aneurysm

MedGen UID:
505953
Concept ID:
CN005832
Finding
 
HPO: HP:0006698

Definition

A localized outpouching of ventricular cavity that is generally associated with dyskinesia and paradoxical expansion during systole. [from HPO]

Conditions with this feature

Arrhythmogenic right ventricular cardiomyopathy, type 2
MedGen UID:
318748
Concept ID:
C1832931
Disease or Syndrome
Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is characterized by progressive fibrofatty replacement of the myocardium that predisposes to ventricular tachycardia and sudden death in young individuals and athletes. It primarily affects the right ventricle; with time, it may also involve the left ventricle. The presentation of disease is highly variable even within families, and some affected individuals may not meet established clinical criteria. The mean age at diagnosis is 31 years (±13; range: 4-64 years).
Arrhythmogenic right ventricular cardiomyopathy, type 9
MedGen UID:
373205
Concept ID:
C1836906
Disease or Syndrome
Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is characterized by progressive fibrofatty replacement of the myocardium that predisposes to ventricular tachycardia and sudden death in young individuals and athletes. It primarily affects the right ventricle; with time, it may also involve the left ventricle. The presentation of disease is highly variable even within families, and some affected individuals may not meet established clinical criteria. The mean age at diagnosis is 31 years (±13; range: 4-64 years).

Recent clinical studies

Etiology

Kiefer TL, Hughes GC, Johnson JC, Harrison JK
Ann Thorac Surg 2014 Jan;97(1):313-5. doi: 10.1016/j.athoracsur.2013.04.130. PMID: 24384180
Finocchiaro G, Murphy D, Pavlovic A, Haddad F, Shiran H, Sinagra G, Ashley EA, Knowles JW
Echocardiography 2014 Mar;31(3):E80-4. Epub 2013 Dec 3 doi: 10.1111/echo.12467. [Epub ahead of print] PMID: 24299065
Luni FK, Moza A, Sheikh M, Coker MF, Chaganti SK, Lewis TJ, Kanjwal Y
Tex Heart Inst J 2013;40(4):465-7. PMID: 24082381Free PMC Article
Tsukui H, Umehara N, Yamazaki K
Heart Vessels 2013 May;28(3):401-3. Epub 2012 Jul 25 doi: 10.1007/s00380-012-0269-y. [Epub ahead of print] PMID: 22828797
Ikeda A, Matsushita S, Sakakibara Y
Thorac Cardiovasc Surg 2012 Dec;60 Suppl 2:e9-12. Epub 2012 Jan 3 doi: 10.1055/s-0031-1295583. [Epub ahead of print] PMID: 22215503

Diagnosis

Baumann S, Renker M, Schoepf UJ, Suranyi P, Harris BS, Varga-Szemes A
Can J Cardiol 2014 Nov;30(11):1463.e1-2. Epub 2014 Jun 30 doi: 10.1016/j.cjca.2014.06.017. [Epub ahead of print] PMID: 25442454
Terada T, Sakurai H, Nonaka T, Sakurai T, Sugiura J, Otsuka R
World J Pediatr Congenit Heart Surg 2014 Oct;5(4):583-5. doi: 10.1177/2150135114542164. PMID: 25324258
Hiraoka A, Totsugawa T, Irisawa Y, Yoshitaka H
J Thorac Cardiovasc Surg 2014 Nov;148(5):2417-8. Epub 2014 Apr 19 doi: 10.1016/j.jtcvs.2014.04.033. [Epub ahead of print] PMID: 24836723
Penkalla A, Solowjowa N, Dandel M, Knosalla C
Eur J Cardiothorac Surg 2014 Aug;46(2):333. Epub 2014 Feb 3 doi: 10.1093/ejcts/ezt590. [Epub ahead of print] PMID: 24493061
Lai WT, Lin SM, Wu SJ, Hwang HK, Peng CC, Chen MR
Pediatr Neonatol 2013 Dec;54(6):406-8. Epub 2013 Jan 21 doi: 10.1016/j.pedneo.2012.12.001. [Epub ahead of print] PMID: 23597547

Therapy

Ozyilmaz I, Saygi M, Yildiz O, Erek E, Guzeltas A
World J Pediatr Congenit Heart Surg 2014 Oct;5(4):637-9. doi: 10.1177/2150135114541860. PMID: 25324272
Fok M, Bashir M, Hammoud I, Harrington D, Kuduvalli M, Field M, Oo A
Ann R Coll Surg Engl 2014 Oct;96(7):e6-7. doi: 10.1308/003588414X13946184900561. PMID: 25245713
Hiraoka A, Totsugawa T, Irisawa Y, Yoshitaka H
J Thorac Cardiovasc Surg 2014 Nov;148(5):2417-8. Epub 2014 Apr 19 doi: 10.1016/j.jtcvs.2014.04.033. [Epub ahead of print] PMID: 24836723
Finocchiaro G, Murphy D, Pavlovic A, Haddad F, Shiran H, Sinagra G, Ashley EA, Knowles JW
Echocardiography 2014 Mar;31(3):E80-4. Epub 2013 Dec 3 doi: 10.1111/echo.12467. [Epub ahead of print] PMID: 24299065
Svensson E, Culig MH, Keenan RJ, Song T, Biederman R
Ann Thorac Surg 2012 Sep;94(3):e63-4. doi: 10.1016/j.athoracsur.2012.02.032. PMID: 22916781

Prognosis

Fok M, Bashir M, Hammoud I, Harrington D, Kuduvalli M, Field M, Oo A
Ann R Coll Surg Engl 2014 Oct;96(7):e6-7. doi: 10.1308/003588414X13946184900561. PMID: 25245713
Nakamura K, Naito S, Oshima S
Europace 2014 Aug;16(8):1225. Epub 2014 Jul 10 doi: 10.1093/europace/euu186. [Epub ahead of print] PMID: 25013010
Purohit M, Gavin N
Asian Cardiovasc Thorac Ann 2014 Mar;22(3):366. Epub 2013 Jul 16 doi: 10.1177/0218492312472515. [Epub ahead of print] PMID: 24585923
Kiefer TL, Hughes GC, Johnson JC, Harrison JK
Ann Thorac Surg 2014 Jan;97(1):313-5. doi: 10.1016/j.athoracsur.2013.04.130. PMID: 24384180
Finocchiaro G, Murphy D, Pavlovic A, Haddad F, Shiran H, Sinagra G, Ashley EA, Knowles JW
Echocardiography 2014 Mar;31(3):E80-4. Epub 2013 Dec 3 doi: 10.1111/echo.12467. [Epub ahead of print] PMID: 24299065

Clinical prediction guides

Terada T, Sakurai H, Nonaka T, Sakurai T, Sugiura J, Otsuka R
World J Pediatr Congenit Heart Surg 2014 Oct;5(4):583-5. doi: 10.1177/2150135114542164. PMID: 25324258
Nakamura K, Naito S, Oshima S
Europace 2014 Aug;16(8):1225. Epub 2014 Jul 10 doi: 10.1093/europace/euu186. [Epub ahead of print] PMID: 25013010
Luni FK, Moza A, Sheikh M, Coker MF, Chaganti SK, Lewis TJ, Kanjwal Y
Tex Heart Inst J 2013;40(4):465-7. PMID: 24082381Free PMC Article
Yu Y, Gao MX, Li HT, Zhang F, Gu CX
Chin Med J (Engl) 2012 Nov;125(21):3836-9. PMID: 23106884
Fujita Y, Hidaka N, Yumoto Y, Morihana E, Fukushima K, Wake N
J Obstet Gynaecol Res 2012 Mar;38(3):586-8. Epub 2012 Feb 22 doi: 10.1111/j.1447-0756.2011.01760.x. [Epub ahead of print] PMID: 22353149

Recent systematic reviews

Raja SG, Salehi S, Bahrami TT
J Card Surg 2009 May-Jun;24(3):319-24. doi: 10.1111/j.1540-8191.2009.00846.x. PMID: 19438791
Parolari A, Naliato M, Loardi C, Denti P, Trezzi M, Zanobini M, Porqueddu M, Roberto M, Kassem S, Alamanni F, Tremoli E, Biglioli P
Ann Thorac Surg 2007 Jun;83(6):2009-16. doi: 10.1016/j.athoracsur.2007.01.032. PMID: 17532388
Johnstone DE, Abdulla A, Arnold JM, Bernstein V, Bourassa M, Brophy J, Davies R, Gardner M, Hoeschen R, Mickleborough L
Can J Cardiol 1994 Jul-Aug;10(6):613-31, 635-54. PMID: 8044722
Kirklin JW, Naftel CD, Blackstone EH, Pohost GM
Circulation 1989 Jun;79(6 Pt 2):I81-91. PMID: 2655982

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