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B Lymphoblastic Leukemia/Lymphoma, Not Otherwise Specified

MedGen UID:
437497
Concept ID:
C2698310
Neoplastic Process
Synonyms: B Lymphoblastic Leukemia/Lymphoma, NOS; B-Lymphoblastic Leukemia/Lymphoma, Not Otherwise Specified

Definition

The term refers to precursor lymphoid neoplasms which are composed of B-lymphoblasts and characterized by the absence of recurrent genetic abnormalities. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • B Lymphoblastic Leukemia/Lymphoma, Not Otherwise Specified

Professional guidelines

PubMed

Temple WC, Mueller S, Hermiston ML, Burkhardt B
Best Pract Res Clin Haematol 2023 Mar;36(1):101449. Epub 2023 Feb 16 doi: 10.1016/j.beha.2023.101449. PMID: 36907639
Eichhorst B, Robak T, Montserrat E, Ghia P, Niemann CU, Kater AP, Gregor M, Cymbalista F, Buske C, Hillmen P, Hallek M, Mey U; ESMO Guidelines Committee. Electronic address: clinicalguidelines@esmo.org
Ann Oncol 2021 Jan;32(1):23-33. Epub 2020 Oct 19 doi: 10.1016/j.annonc.2020.09.019. PMID: 33091559
Ferry JA
Oncologist 2006 Apr;11(4):375-83. doi: 10.1634/theoncologist.11-4-375. PMID: 16614233

Recent clinical studies

Etiology

Radkiewicz C, Bruchfeld JB, Weibull CE, Jeppesen ML, Frederiksen H, Lambe M, Jakobsen L, El-Galaly TC, Smedby KE, Wästerlid T
Am J Hematol 2023 Jan;98(1):23-30. Epub 2022 Oct 10 doi: 10.1002/ajh.26744. PMID: 36178436Free PMC Article
Maeshima AM, Taniguchi H, Hattori D, Sasaki H, Hori Y, Makita S, Iwaki N, Fukuhara S, Munakata W, Suzuki T, Izutsu K
Hum Pathol 2022 Jun;124:14-23. Epub 2022 Mar 17 doi: 10.1016/j.humpath.2022.03.005. PMID: 35307403
Khanlari M, Medeiros LJ, Lin P, Xu J, You MJ, Tang G, Yin CC, Wang W, Qiu L, Miranda RN, Bueso-Ramos CE, Li S
Mod Pathol 2022 Mar;35(3):419-426. Epub 2021 Oct 4 doi: 10.1038/s41379-021-00909-4. PMID: 34608246
de Arruda JAA, Schuch LF, Conte Neto N, de Souza LL, Rodrigues-Fernandes CI, Abreu LG, Soares CD, de Carvalho MGF, Agostini M, de Andrade BAB, Romañach MJ, Zanella VG, Barra MB, Martins MD, Souto GR, Etges A, Pontes HAR, Pontes FSC, Vargas PA, de Almeida OP, Santos-Silva AR, Lopes MA, Pires FR, Gomez RS, Fonseca FP, Mesquita RA
J Oral Pathol Med 2021 Jul;50(6):603-612. Epub 2021 Jun 30 doi: 10.1111/jop.13211. PMID: 34091952
Konoplev S, Lu X, Konopleva M, Jain N, Ouyang J, Goswami M, Roberts KG, Valentine M, Mullighan CG, Bueso-Ramos C, Zweidler-McKay PA, Jorgensen JL, Wang SA
Am J Clin Pathol 2017 Apr 1;147(4):357-363. doi: 10.1093/ajcp/aqx005. PMID: 28340183

Diagnosis

Maeshima AM, Taniguchi H, Hattori D, Sasaki H, Hori Y, Makita S, Iwaki N, Fukuhara S, Munakata W, Suzuki T, Izutsu K
Hum Pathol 2022 Jun;124:14-23. Epub 2022 Mar 17 doi: 10.1016/j.humpath.2022.03.005. PMID: 35307403
de Arruda JAA, Schuch LF, Conte Neto N, de Souza LL, Rodrigues-Fernandes CI, Abreu LG, Soares CD, de Carvalho MGF, Agostini M, de Andrade BAB, Romañach MJ, Zanella VG, Barra MB, Martins MD, Souto GR, Etges A, Pontes HAR, Pontes FSC, Vargas PA, de Almeida OP, Santos-Silva AR, Lopes MA, Pires FR, Gomez RS, Fonseca FP, Mesquita RA
J Oral Pathol Med 2021 Jul;50(6):603-612. Epub 2021 Jun 30 doi: 10.1111/jop.13211. PMID: 34091952
Zamò A, Johnston P, Attygalle AD, Laurent C, Arber DA, Fend F
Histopathology 2020 Sep;77(3):369-379. Epub 2020 Jul 14 doi: 10.1111/his.14124. PMID: 32324290
Loghavi S, Kutok JL, Jorgensen JL
Am J Clin Pathol 2015 Sep;144(3):393-410. doi: 10.1309/AJCPAN7BH5DNYWZB. PMID: 26276770
Waibel M, Gregory G, Shortt J, Johnstone RW
Curr Opin Hematol 2014 Jul;21(4):297-308. doi: 10.1097/MOH.0000000000000045. PMID: 24811162

Therapy

Fujihara M, Sakata R, Yoshida N, Ozasa K, Preston DL, Mabuchi K
Blood 2022 Jan 13;139(2):217-227. doi: 10.1182/blood.2020010475. PMID: 34428282Free PMC Article
Hastings C, Chen Y, Devidas M, Ritchey AK, Winick NJ, Carroll WL, Hunger SP, Wood BL, Marcus RB, Barredo JC
Pediatr Blood Cancer 2021 Dec;68(12):e29256. Epub 2021 Jul 24 doi: 10.1002/pbc.29256. PMID: 34302704Free PMC Article
Lee A
Drugs 2021 Jul;81(10):1229-1233. doi: 10.1007/s40265-021-01550-w. PMID: 34143407
Al Mahmoud R, Weitzman S, Schechter T, Ngan B, Abdelhaleem M, Alexander S
J Pediatr Hematol Oncol 2012 Nov;34(8):611-6. doi: 10.1097/MPH.0b013e3182707592. PMID: 23042011
Takamatsu Y, Suzumiya J, Utsunomiya A, Maeda K, Matsuoka H, Suzushima H, Tsukada J, Shibata K, Tamura K; Kyushu Hematology Organization for Treatment Study Group (K-HOT)
Eur J Haematol 2010 May;84(5):391-7. Epub 2010 Jan 5 doi: 10.1111/j.1600-0609.2010.01411.x. PMID: 20059527

Prognosis

Satoh T, Kayano H, Kohri M, Tanae K, Asou C, Takahashi N, Tsukasaki K, Yasuda M
J Clin Exp Hematop 2023;63(4):257-261. doi: 10.3960/jslrt.23042. PMID: 38148016Free PMC Article
Radkiewicz C, Bruchfeld JB, Weibull CE, Jeppesen ML, Frederiksen H, Lambe M, Jakobsen L, El-Galaly TC, Smedby KE, Wästerlid T
Am J Hematol 2023 Jan;98(1):23-30. Epub 2022 Oct 10 doi: 10.1002/ajh.26744. PMID: 36178436Free PMC Article
Khanlari M, Medeiros LJ, Lin P, Xu J, You MJ, Tang G, Yin CC, Wang W, Qiu L, Miranda RN, Bueso-Ramos CE, Li S
Mod Pathol 2022 Mar;35(3):419-426. Epub 2021 Oct 4 doi: 10.1038/s41379-021-00909-4. PMID: 34608246
Maeshima AM, Taniguchi H, Ida H, Hosoba R, Fujino T, Saito Y, Yuda S, Makita S, Fukuhara S, Munakata W, Suzuki T, Maruyama D, Izutsu K
Hum Pathol 2020 Aug;102:33-43. Epub 2020 Jun 12 doi: 10.1016/j.humpath.2020.06.001. PMID: 32540222
Al Mahmoud R, Weitzman S, Schechter T, Ngan B, Abdelhaleem M, Alexander S
J Pediatr Hematol Oncol 2012 Nov;34(8):611-6. doi: 10.1097/MPH.0b013e3182707592. PMID: 23042011

Clinical prediction guides

Radkiewicz C, Bruchfeld JB, Weibull CE, Jeppesen ML, Frederiksen H, Lambe M, Jakobsen L, El-Galaly TC, Smedby KE, Wästerlid T
Am J Hematol 2023 Jan;98(1):23-30. Epub 2022 Oct 10 doi: 10.1002/ajh.26744. PMID: 36178436Free PMC Article
Siegele BJ, Stemmer-Rachamimov AO, Lilljebjorn H, Fioretos T, Winters AC, Dal Cin P, Treece A, Gaskell A, Nardi V
Genes Chromosomes Cancer 2022 Aug;61(8):449-458. Epub 2022 Mar 7 doi: 10.1002/gcc.23033. PMID: 35218117
Khanlari M, Medeiros LJ, Lin P, Xu J, You MJ, Tang G, Yin CC, Wang W, Qiu L, Miranda RN, Bueso-Ramos CE, Li S
Mod Pathol 2022 Mar;35(3):419-426. Epub 2021 Oct 4 doi: 10.1038/s41379-021-00909-4. PMID: 34608246
Szumera-Ciećkiewicz A, Wojciechowska U, Didkowska J, Poleszczuk J, Rymkiewicz G, Paszkiewicz-Kozik E, Sokół K, Prochorec-Sobieszek M, Walewski J
Sci Rep 2020 Sep 3;10(1):14610. doi: 10.1038/s41598-020-71579-6. PMID: 32884080Free PMC Article
Maeshima AM, Taniguchi H, Ida H, Hosoba R, Fujino T, Saito Y, Yuda S, Makita S, Fukuhara S, Munakata W, Suzuki T, Maruyama D, Izutsu K
Hum Pathol 2020 Aug;102:33-43. Epub 2020 Jun 12 doi: 10.1016/j.humpath.2020.06.001. PMID: 32540222

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