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Superior vena cava angiosarcoma

MedGen UID:
234373
•Concept ID:
C1336530
•
Neoplastic Process
Synonyms: angiosarcoma (disease) of anterior vena cava; Angiosarcoma of Superior Vena Cava; angiosarcoma of Superior vena cava; Angiosarcoma of the Superior Vena Cava; angiosarcoma of the Superior vena cava; anterior vena cava angiosarcoma (disease); Superior Vena Cava Angiosarcoma; superior vena cava angiosarcoma
 
Monarch Initiative: MONDO:0003032

Definition

A malignant vascular neoplasm arising from the superior vena cava. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSuperior vena cava angiosarcoma

Recent clinical studies

Etiology

Percutaneous endovascular tissue sampling of endoluminal tumors using directional atherectomy.
Massmann A, Seidel R, Schneider GK, Buecker A, Fries P
Eur Radiol 2019 Sep;29(9):5007-5012. Epub 2019 Feb 22 doi: 10.1007/s00330-019-06015-z. PMID: 30796569
Detecting cardiac involvement in sarcoidosis: a call for prospective studies of newer imaging techniques.
Pandya C, Brunken RC, Tchou P, Schoenhagen P, Culver DA
Eur Respir J 2007 Feb;29(2):418-22. doi: 10.1183/09031936.00076406. PMID: 17264327
Non-myxomatous cardiac tumours: twenty-year experience.
Mathur A, Airan B, Bhan A, Sharma R, Sampath Kumar A, Talwar KK, Chopra P, Venugopal P
Indian Heart J 2000 May-Jun;52(3):319-23. PMID: 10976154

Diagnosis

If not angioedema, what is it? Diagnostic approach to facial edema.
Velasco-Amador JP, Prados-Carmona Á, Navarro-Triviño FJ
J Dtsch Dermatol Ges 2024 Apr;22(4):501-512. Epub 2024 Mar 14 doi: 10.1111/ddg.15336. PMID: 38483055
Primary angiosarcoma of superior vena cava: an unexpected diagnosis after an oncological emergency.
Rêgo Salgueiro F, Vieira I, Gomes I, Petrova M
BMJ Case Rep 2021 Apr 16;14(4) doi: 10.1136/bcr-2020-241266. PMID: 33863773Free PMC Article
Percutaneous endovascular tissue sampling of endoluminal tumors using directional atherectomy.
Massmann A, Seidel R, Schneider GK, Buecker A, Fries P
Eur Radiol 2019 Sep;29(9):5007-5012. Epub 2019 Feb 22 doi: 10.1007/s00330-019-06015-z. PMID: 30796569
Angiosarcoma of the right atrium with extension to the superior and inferior vena cavae.
Cetinkaya A, Skwara W, Hein S, Bramlage P, Schönburg M, Richter M
J Card Surg 2018 Dec;33(12):806-807. Epub 2018 Dec 11 doi: 10.1111/jocs.13964. PMID: 30537242
Cardiac angiosarcoma--a review.
Murinello A, Mendonça P, Abreu A, Santos AL, Roquete J, Pinto E, Alpendra J, Semedo J, Rodrigues A, Cunha D, Coelho JF, Lourenço S, Miranda S
Rev Port Cardiol 2007 May;26(5):577-84. PMID: 17691282

Therapy

Improved outcome with multimodality therapy in primary cardiac angiosarcoma.
Pigott C, Welker M, Khosla P, Higgins RS
Nat Clin Pract Oncol 2008 Feb;5(2):112-5. doi: 10.1038/ncponc1023. PMID: 18235443
Primary heart angiosarcoma detected by computed tomography and magnetic resonance imaging.
Bruna J, Lockwood M
Eur Radiol 1998;8(1):66-8. doi: 10.1007/s003300050341. PMID: 9442133

Prognosis

Perigraft hygroma mimicking recurrent angiosarcoma of the right atrium.
Ko K, Evers J, Smith T, Morshuis WJ, Geuzebroek GSC
Gen Thorac Cardiovasc Surg 2022 Feb;70(2):184-189. Epub 2021 Nov 17 doi: 10.1007/s11748-021-01737-8. PMID: 34787734
Primary angiosarcoma of superior vena cava: an unexpected diagnosis after an oncological emergency.
Rêgo Salgueiro F, Vieira I, Gomes I, Petrova M
BMJ Case Rep 2021 Apr 16;14(4) doi: 10.1136/bcr-2020-241266. PMID: 33863773Free PMC Article
Percutaneous endovascular tissue sampling of endoluminal tumors using directional atherectomy.
Massmann A, Seidel R, Schneider GK, Buecker A, Fries P
Eur Radiol 2019 Sep;29(9):5007-5012. Epub 2019 Feb 22 doi: 10.1007/s00330-019-06015-z. PMID: 30796569
Large right atrial angiosarcoma with superior vena cava obstruction and cardiovascular collapse.
Jiang L, Luo T, Leong K
Hellenic J Cardiol 2016 Sep-Oct;57(5):355-358. Epub 2016 Nov 15 doi: 10.1016/j.hjc.2016.11.028. PMID: 28202217
Cardiac angiosarcoma--a review.
Murinello A, Mendonça P, Abreu A, Santos AL, Roquete J, Pinto E, Alpendra J, Semedo J, Rodrigues A, Cunha D, Coelho JF, Lourenço S, Miranda S
Rev Port Cardiol 2007 May;26(5):577-84. PMID: 17691282

Clinical prediction guides

Localization of angiosarcoma by peri-operative transesophageal echocardiography.
Chen YC
Int J Cardiovasc Imaging 2017 Nov;33(11):1749-1751. Epub 2017 Jun 7 doi: 10.1007/s10554-017-1183-2. PMID: 28593398
Detecting cardiac involvement in sarcoidosis: a call for prospective studies of newer imaging techniques.
Pandya C, Brunken RC, Tchou P, Schoenhagen P, Culver DA
Eur Respir J 2007 Feb;29(2):418-22. doi: 10.1183/09031936.00076406. PMID: 17264327

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