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    PMS1 PMS1 postmeiotic segregation increased 1 (S. cerevisiae) [ Homo sapiens ]

    Gene ID: 5378, updated on 20-May-2012

    Summary

    Official Symbol
    PMS1provided by HGNC
    Official Full Name
    PMS1 postmeiotic segregation increased 1 (S. cerevisiae)provided by HGNC
    Primary source
    HGNC:9121
    See related
    Ensembl:ENSG00000064933; HPRD:02597; MIM:600258; Vega:OTTHUMG00000132664
    Gene type
    protein coding
    RefSeq status
    REVIEWED
    Organism
    Homo sapiens
    Lineage
    Eukaryota; Metazoa; Chordata; Craniata; Vertebrata; Euteleostomi; Mammalia; Eutheria; Euarchontoglires; Primates; Haplorrhini; Catarrhini; Hominidae; Homo
    Also known as
    PMSL1; hPMS1; HNPCC3; FLJ98259; DKFZp781M0253
    Summary
    This gene encodes a protein belonging to the DNA mismatch repair mutL/hexB family. This protein is thought to be involved in the repair of DNA mismatches, and it can form heterodimers with MLH1, a known DNA mismatch repair protein. Mutations in this gene cause hereditary nonpolyposis colorectal cancer type 3 (HNPCC3) either alone or in combination with mutations in other genes involved in the HNPCC phenotype, which is also known as Lynch syndrome. [provided by RefSeq, Jul 2008]

    Genomic context

    Location :
    2q31.1
    Sequence :
    Chromosome: 2; NC_000002.11 (190648811..190742355)
    See PMS1 in Epigenomics, MapViewer

    Chromosome 2 - NC_000002.11Genomic Context describing neighboring genes Neighboring gene ankyrin and armadillo repeat containing Neighboring gene O-sialoglycoprotein endopeptidase-like 1 Neighboring gene ORM1-like 1 (S. cerevisiae) Neighboring gene glucosamine-phosphate N-acetyltransferase 1 pseudogene Neighboring gene telomeric repeat binding factor (NIMA-interacting) 1 pseudogene Neighboring gene heterogeneous nuclear ribonucleoprotein C (C1/C2) pseudogene

    Genomic regions, transcripts, and products

    Bibliography

    GeneRIFs: Gene References Into Functions What's a GeneRIF?

    Interactions

    Products Interactant Other Gene Complex Source Pubs Description
    NP_000525.1 NP_000240.1 MLH1    BIND  PubMed hPMS1 interacts with hMLH1. 
    NP_000525.1     BIND  PubMed hPMS1 interacts with hMutS-alpha 
    P54277 P40692 MLH1    HPRD  PubMed  
    BioGRID:111391 BioGRID:115445 AKAP9    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:107027 ATR    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:107142 BRCA2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:123841 BRIP1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:107343 CCNT1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:107424 CDC5L    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:107459 CDK9    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114032 CUL1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114030 CUL3    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:107920 CYLD    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114602 EXO1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:116573 FAN1    BioGRID  PubMed Affinity Capture-MS 
    BioGRID:111391 BioGRID:124978 HELB    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114438 HERC2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110041 IPO5    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:120830 IPO9    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110036 KPNA2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110343 MCM6    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110438 MLH1    BioGRID  PubMed Affinity Capture-MS; Affinity Capture-Western; Co-localization; Two-hybrid 
    BioGRID:111391 BioGRID:122103 MMS19    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110484 MOV10    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110573 MSH2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:109211 MSH6    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:110904 NONO    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111251 PGK1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111304 PIK3C2A    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111391 PMS1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114909 POLR1C    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111510 PPP2R1A    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:123977 PSD2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111673 PSMC1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:115359 RANBP9    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111840 RANGAP1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111912 REV3L    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111913 RFC1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111914 RFC2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:111916 RFC4    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:121971 RNF123    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:121119 RNF20    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:112212 SBF1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:123597 SBF2    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114574 SMC3    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:113003 TOP1    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:115227 UBAP2L    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:113164 UBC    BioGRID  PubMed Affinity Capture-MS; Affinity Capture-Western 
    BioGRID:111391 BioGRID:119501 UBR5    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:114465 USP13    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:113751 USP5    BioGRID  PubMed Affinity Capture-Western 
    BioGRID:111391 BioGRID:113892 USP9Y    BioGRID  PubMed Affinity Capture-Western 

    General gene information

    Markers

    Homology

    Gene Ontology Provided by GOA

    Function Evidence Code Pubs
    ATP binding IEA
    Inferred from Electronic Annotation
    more info
     
    ATPase activity IBA
    Inferred from Biological aspect of Ancestor
    more info
     
    DNA binding IEA
    Inferred from Electronic Annotation
    more info
     
    mismatched DNA binding IBA
    Inferred from Biological aspect of Ancestor
    more info
     
    mismatched DNA binding IEA
    Inferred from Electronic Annotation
    more info
     
    Process Evidence Code Pubs
    ATP catabolic process IBA
    Inferred from Biological aspect of Ancestor
    more info
     
    mismatch repair IBA
    Inferred from Biological aspect of Ancestor
    more info
     
    mismatch repair IEA
    Inferred from Electronic Annotation
    more info
     
    reciprocal meiotic recombination IBA
    Inferred from Biological aspect of Ancestor
    more info
     
    Component Evidence Code Pubs
    MutLalpha complex IBA
    Inferred from Biological aspect of Ancestor
    more info
     
    nucleus IEA
    Inferred from Electronic Annotation
    more info
     

    General protein information

    Preferred Names
    PMS1 protein homolog 1
    Names
    PMS1 protein homolog 1
    mismatch repair gene PMSL1
    human homolog of yeast mutL
    DNA mismatch repair protein PMS1
    rhabdomyosarcoma antigen MU-RMS-40.10B
    rhabdomyosarcoma antigen MU-RMS-40.10E

    NCBI Reference Sequences (RefSeq)

    RefSeqs maintained independently of Annotated Genomes

    These reference sequences exist independently of genome builds. Explain

    These reference sequences are curated independently of the genome annotation cycle, so their versions may not match the RefSeq versions in the current genome build. Identify version mismatches by comparing the version of the RefSeq in this section to the one reported in Genomic regions, transcripts, and products above.

    Genomic

    1. NG_008648.1 RefSeqGene

      Range
      5001..98545
      Download
      GenBank, FASTA, Sequence Viewer (Graphics)

    mRNA and Protein(s)

    1. NM_000534.4NP_000525.1  PMS1 protein homolog 1 isoform a

      Status: REVIEWED

      Description
      Transcript Variant: This variant (1) represents the longest transcript and encodes the longest isoform (a).
      Source sequence(s)
      BC096330, BC096332, BM677668, DC347859
      Consensus CDS
      CCDS2302.1
      UniProtKB/Swiss-Prot
      P54277
      Related
      ENSP00000406490, OTTHUMP00000163499, ENST00000441310, OTTHUMT00000255918
      Conserved Domains (4) summary
      cd01390
      Location:572636
      Blast Score: 115
      HMGB-UBF_HMG-box; HMGB-UBF_HMG-box, class II and III members of the HMG-box superfamily of DNA-binding proteins. These proteins bind the minor groove of DNA in a non-sequence specific fashion and contain two or more tandem HMG boxes. Class II members include non-histone ...
      cd03485
      Location:205338
      Blast Score: 414
      MutL_Trans_hPMS_1_like; MutL_Trans_hPMS1_like: transducer domain, having a ribosomal S5 domain 2-like fold, found in proteins similar to human PSM1 (hPSM1) and yeast MLH2. hPSM1 and yMLH2 are members of the DNA mismatch repair (MutL/MLH1/PMS2) family. This transducer domain is ...
      TIGR00585
      Location:1318
      Blast Score: 886
      mutl; DNA mismatch repair protein MutL
      cl00075
      Location:27124
      Blast Score: 128
      HATPase_c; Histidine kinase-like ATPases; This family includes several ATP-binding proteins for example: histidine kinase, DNA gyrase B, topoisomerases, heat shock protein HSP90, phytochrome-like ATPases and DNA mismatch repair proteins
    2. NM_001128143.1NP_001121615.1  PMS1 protein homolog 1 isoform b

      Status: REVIEWED

      Description
      Transcript Variant: This variant (2, also known as PMS1 nirs variant 7) lacks an alternate in-frame exon in the mid-coding region, compared to variant 1, resulting in a shorter protein (isoform b), compared to isoform a.
      Source sequence(s)
      AB102875, BM677668, DC347859
      Consensus CDS
      CCDS46474.1
      Related
      ENSP00000387125, OTTHUMP00000205717, ENST00000409823, OTTHUMT00000335283
      Conserved Domains (4) summary
      cd01390
      Location:533597
      Blast Score: 115
      HMGB-UBF_HMG-box; HMGB-UBF_HMG-box, class II and III members of the HMG-box superfamily of DNA-binding proteins. These proteins bind the minor groove of DNA in a non-sequence specific fashion and contain two or more tandem HMG boxes. Class II members include non-histone ...
      cd03485
      Location:194299
      Blast Score: 320
      MutL_Trans_hPMS_1_like; MutL_Trans_hPMS1_like: transducer domain, having a ribosomal S5 domain 2-like fold, found in proteins similar to human PSM1 (hPSM1) and yeast MLH2. hPSM1 and yMLH2 are members of the DNA mismatch repair (MutL/MLH1/PMS2) family. This transducer domain is ...
      TIGR00585
      Location:1279
      Blast Score: 787
      mutl; DNA mismatch repair protein MutL
      cl00075
      Location:27124
      Blast Score: 128
      HATPase_c; Histidine kinase-like ATPases; This family includes several ATP-binding proteins for example: histidine kinase, DNA gyrase B, topoisomerases, heat shock protein HSP90, phytochrome-like ATPases and DNA mismatch repair proteins
    3. NM_001128144.1NP_001121616.1  PMS1 protein homolog 1 isoform c

      Status: REVIEWED

      Description
      Transcript Variant: This variant (3, also known as PMS1 nirs variant 2) lacks an alternate in-frame exon in the 3' coding region, compared to variant 1, resulting in a shorter protein (isoform c), compared to isoform a.
      Source sequence(s)
      AB102870, BC096330, BM677668, DC347859
      Consensus CDS
      CCDS46473.1
      UniProtKB/Swiss-Prot
      P54277
      Related
      ENSP00000401064, OTTHUMP00000205724, ENST00000447232, OTTHUMT00000335290
      Conserved Domains (4) summary
      cd01390
      Location:572617
      Blast Score: 134
      HMGB-UBF_HMG-box; HMGB-UBF_HMG-box, class II and III members of the HMG-box superfamily of DNA-binding proteins. These proteins bind the minor groove of DNA in a non-sequence specific fashion and contain two or more tandem HMG boxes. Class II members include non-histone ...
      cd03485
      Location:205338
      Blast Score: 418
      MutL_Trans_hPMS_1_like; MutL_Trans_hPMS1_like: transducer domain, having a ribosomal S5 domain 2-like fold, found in proteins similar to human PSM1 (hPSM1) and yeast MLH2. hPSM1 and yMLH2 are members of the DNA mismatch repair (MutL/MLH1/PMS2) family. This transducer domain is ...
      TIGR00585
      Location:1318
      Blast Score: 887
      mutl; DNA mismatch repair protein MutL
      cl00075
      Location:27124
      Blast Score: 127
      HATPase_c; Histidine kinase-like ATPases; This family includes several ATP-binding proteins for example: histidine kinase, DNA gyrase B, topoisomerases, heat shock protein HSP90, phytochrome-like ATPases and DNA mismatch repair proteins

    RefSeqs of Annotated Genomes: Build 37.3

    The following sections contain reference sequences that belong to a specific genome build. Explain

    Reference GRCh37.p5 Primary Assembly

    Genomic

    1. NC_000002.11 Reference GRCh37.p5 Primary Assembly

      Range
      190648811..190742355
      Download
      GenBank, FASTA, Sequence Viewer (Graphics)

    Alternate HuRef

    Genomic

    1. AC_000134.1 Alternate HuRef

      Range
      182508462..182602272
      Download
      GenBank, FASTA, Sequence Viewer (Graphics)

    Related Sequences

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