| Disorder | Symbol(s) | OMIM | Location |
| Deafness, Y-linked 1 (1) | DFNY1 | 400043 |
Chr.Y |
| Deafness, autosomal dominant 1, 124900 (3) | DIAPH1, DFNA1, LFHL1 | 602121 |
5q31 |
| Deafness, autosomal dominant 10, 601316 (3) | EYA4, DFNA10, CMD1J | 603550 |
6q23 |
| Deafness, autosomal dominant 11, neurosensory, 601317 (3) | MYO7A, USH1B, DFNB2, DFNA11 | 276903 |
11q13.5 |
| Deafness, autosomal dominant 13, 601868 (3) | COL11A2, STL3, DFNA13, DFNB53 | 120290 |
6p21.3 |
| Deafness, autosomal dominant 15, 602459 (3) | POU4F3, BRN3C | 602460 |
5q31 |
| Deafness, autosomal dominant 16 (2) | DFNA16 | 603964 |
2q23-q24.3 |
| Deafness, autosomal dominant 17, 603622 (3) | MYH9, MHA, FTNS, DFNA17 | 160775 |
22q11.2 |
| Deafness, autosomal dominant 18 (2) | DFNA18 | 606012 |
3q22 |
| Deafness, autosomal dominant 20/26, 604717 (3) | ACTG1, DFNA20, DFNA26 | 102560 |
17q25.3 |
| Deafness, autosomal dominant 21 (2) | DFNA21 | 607017 |
6p21.3 |
| Deafness, autosomal dominant 22, 606346 (3) | MYO6, DFNA22, DFNB37 | 600970 |
6q13 |
| Deafness, autosomal dominant 23, 605192 (3) | SIX1, BOS3, DFNA23 | 601205 |
14q23 |
| Deafness, autosomal dominant 24 (2) | DFNA24 | 606282 |
4q35-qter |
| Deafness, autosomal dominant 25, 605583 (3) | SLC17A8, VGLUT3, DFNA25 | 607557 |
12q23 |
| Deafness, autosomal dominant 27 (2) | DFNA27 | 612431 |
4q12-q13.1 |
| Deafness, autosomal dominant 28, 608641 (3) | GRHL2, TFCP2L3, DFNA28 | 608576 |
8q22 |
| Deafness, autosomal dominant 2A, 600101 (3) | KCNQ4, DFNA2A | 603537 |
1p34 |
| Deafness, autosomal dominant 2B, 612644 (3) | GJB3, CX31, DFNA2B | 603324 |
1p35.1 |
| Deafness, autosomal dominant 30 (2) | DFNA30 | 606451 |
15q25-q26 |